Ernst Conzelmann

University of Würzburg — Germany

Medicine · Health Sciences

38h-index5.5kcitations88works0.02yr avg
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Research Topics

Lysosomal Storage Disorders Research(43), Glycosylation and Glycoproteins Research(29), Peroxisome Proliferator-Activated Receptors(17), Metabolism and Genetic Disorders(15), Cellular transport and secretion(10)

Publications88 total

Peroxisomal membrane channel Pxmp2 in the mammary fat pad is essential for stromal lipid homeostasis and for development of mammary gland epithelium in mice
Developmental Biology·2014· 28 cited
Metabolic adaptation allows Amacr-deficient mice to remain symptom-free despite low levels of mature bile acids
Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids·2013· 12 cited
The Enolization Chemistry of a Thioester-Dependent Racemase: The 1.4 Å Crystal Structure of a Reaction Intermediate Complex Characterized by Detailed QM/MM Calculations
The Journal of Physical Chemistry B·2012· 19 cited
Mitochondrial 2,4-dienoyl-CoA Reductase Deficiency in Mice Results in Severe Hypoglycemia with Stress Intolerance and Unimpaired Ketogenesis
PLoS Genetics·2009· 61 citedOpen Access
Proteomic analysis of cathepsin B and L-deficient mouse brain lysosomes
Biochimica et Biophysica Acta (BBA) - Proteins and Proteomics·2007· 60 citedOpen Access
The Catalysis of the 1,1-Proton Transfer by α-Methyl-acyl-CoA Racemase Is Coupled to a Movement of the Fatty Acyl Moiety Over a Hydrophobic, Methionine-rich Surface
Journal of Molecular Biology·2007· 41 cited
The human IgM antibody SAM-6 induces tumor-specific apoptosis with oxidized low-density lipoprotein
Molecular Cancer Therapeutics·2007· 59 cited
α-Methylacyl-CoA Racemase from Mycobacterium tuberculosis
Journal of Biological Chemistry·2005· 49 citedOpen Access
Alpha-methylacyl-CoA racemase from Mycobacterium tuberculosis- mutational and structural characterization of the fold and active site
2004
A mouse model for α-methylacyl-CoA racemase deficiency: adjustment of bile acid synthesis and intolerance to dietary methyl-branched lipids
Human Molecular Genetics·2004· 82 citedOpen Access
Elevated α-Methylacyl-CoA Racemase Enzymatic Activity in Prostate Cancer
American Journal Of Pathology·2004· 79 citedOpen Access
Mutations in VKORC1 cause warfarin resistance and multiple coagulation factor deficiency type 2
Nature·2004· 1.1k cited
Crystallization and preliminary X-ray diffraction studies of an α-methylacyl-CoA racemase from<i>Mycobacterium tuberculosis</i>
Acta Crystallographica Section D Biological Crystallography·2003· 18 cited
Defects in degradation of blood group A and B glycosphingolipids in Schindler and Fabry diseases
Journal of Lipid Research·2002· 35 citedOpen Access
PEX1 Mutations in Complementation Group 1 of Zellweger Spectrum Patients Correlate with Severity of Disease
Pediatric Research·2002· 65 cited
The role of α-methylacyl-CoA racemase in bile acid synthesis
Biochemical Journal·2002· 38 citedOpen Access
The role of α-methylacyl-CoA racemase in bile acid synthesis
Biochemical Journal·2002· 21 cited
In Mouse α-Methylacyl-CoA Racemase, the Same Gene Product Is Simultaneously Located in Mitochondria and Peroxisomes
Journal of Biological Chemistry·2000· 59 citedOpen Access
Determination of Urinary Sulfatides and Other Lipids by Combination of Reversed-Phase and Thin-Layer Chromatographies
Analytical Biochemistry·1999· 34 cited
Prenatal diagnosis of X-linked adrenoleukodystrophy combining biochemical, immunocytochemical and DNA analyses
Prenatal Diagnosis·1999· 16 cited
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Frequent Co-authors

Konrad Sandhoff(23), Werner Schmitz(13), J. Kalervo Hiltunen(8), Josef Burg(5), Heidi NEHRKORN(4), Peter Propping(4), Ralph Fingerhut(3), Heli Helander(3), Mary Lee-Vaupel(3), Kalle Savolainen(3), Tiina Kotti(3), Waltraut Friedl(3), P. Leinekugel(2), Günter Schwarzmann(2), Reinhard Schneider(2), Jutta Gärtner(2), Raija Sormunen(2), Abdül Waheed(2), Prasenjit Bhaumik(2), Rik K. Wierenga(2)