Brian S. Appleby

University Hospitals of Cleveland — United States

Biochemistry, Genetics and Molecular Biology · Life Sciences

42h-index5.7kcitations235works3.72yr avg
OpenAlex↗ORCID↗Google Scholar↗Lab page↗

Accepting Students?

No reports yet. Know if this professor is taking students?

Research Topics

Prion Diseases and Protein Misfolding(130), Neurological diseases and metabolism(64), Dementia and Cognitive Impairment Research(39), Amyotrophic Lateral Sclerosis Research(35), Alzheimer's disease research and treatments(34)

Publications234 total

Continuous At-Home Monitoring of Nighttime Bed Behavior in Frontotemporal Dementia
Neurology Open Access·2026
Individualized Atrophy‐Based Prediction of Dementia Progression in Familial Frontotemporal Lobar Degeneration With Bayesian Linear Mixed‐Effects Modeling
Annals of Neurology·2026Open Access
Enhanced Sensitivity of a Modified Quaking‐Induced Conversion Diagnostic Test for the Broad Detection of Sporadic and Inherited Prion Diseases: A Retrospective Study
Annals of Neurology·2026Open Access
Genetic Creutzfeldt-Jakob disease linked to the E200K mutation: a large cohort study
Acta Neuropathologica·2026Open Access
The Phenotypic Spectrum of Sporadic Creutzfeldt‐Jakob Disease Cortical Subtype
Annals of Neurology·2025Open Access
Female Informants are associated with higher CDR PLUS NACC‐FTLD scores in patients with Frontotemporal Dementia
Alzheimer s & Dementia·2025Open Access
Palliative Care Resource Utilization in Patients with Prion Disease
Alzheimer s & Dementia·2025Open Access
Demographic Features of Cleveland Alzheimer's Disease Research Center Participants Who Were Initially Undecided or Change Their Mind Regarding Brain Donation
Alzheimer s & Dementia·2025Open Access
Sex Differences in Neuropsychiatric Symptoms Associated with Agitation in Frontotemporal Lobar Degeneration
Alzheimer s & Dementia·2025Open Access
Caregiver Burden in Prion Disease
Dementia and Geriatric Cognitive Disorders Extra·2025Open Access
Neuropsychiatric symptoms are part of the diagnostic criteria for sporadic Creutzfeldt-Jakob disease
Brain·2025
Mortality of individuals with antemortem genetic testing for <i>PRNP</i> variants in the United States, 1998-2024
2025· 1 citedOpen Access
Development of a user guide to support administration of the MRC Prion Disease Rating Scale in research and clinical settings for prion diseases
Prion·2025Open Access
Functional Connectivity Associations With Markers of Disease Progression in <i>GRN</i> Pathogenic Variant Carriers
Annals of Clinical and Translational Neurology·2025Open Access
Palliative Care Resource Utilization in Patients With Prion Disease
Neurology·2025Open Access
Understanding brain donation decisions: Predictors of indecision and change over time from the Cleveland Alzheimer's Disease Research Center
Alzheimer s & Dementia·2025Open Access
Diagnostic Journey and Health Care Burden of Patients With Creutzfeldt-Jakob Disease in the United States
Neurology Clinical Practice·2025Open Access
Variably protease-sensitive prionopathy: mass spectrometry analysis of the pathogenic prion protein provides a new perspective
Acta Neuropathologica Communications·2025Open Access
Search for a genetic cause of variably protease-sensitive prionopathy
PLoS Pathogens·2025· 2 citedOpen Access
Diagnostic Journey and Health Care Burden of Patients With Creutzfeldt-Jakob Disease in the United States
Neurology Clinical Practice·2025· 1 citedOpen Access
page 1 of 12Next →

Frequent Co-authors

Pierluigi Gambetti(14), Hilary W. Heuer(14), John Kornak(14), Adam L. Boxer(14), Ging‐Yuek Robin Hsiung(14), Edward D. Huey(14), Irene Litvan(14), Ian R. Mackenzie(14), Mario F. Mendez(14), Maria Carmela Tartaglia(14), Danielle Brushaber(13), Julie A. Fields(13), Leah K. Forsberg(13), Bradley F. Boeve(13), Kimiko Domoto‐Reilly(13), Nupur Ghoshal(13), Daniel Kaufer(13), Katya Rascovsky(13), Erik D. Roberson(13), Sandra Weıntraub(13)