Justin Buttner

Hospital for Sick Children — Canada

Medicine · Health Sciences

4h-index624citations6works0.02yr avg
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Research Topics

Lysosomal Storage Disorders Research(5), Glycosylation and Glycoproteins Research(3), Carbohydrate Chemistry and Synthesis(2), Trypanosoma species research and implications(2), Cellular transport and secretion(1)

Publications6 total

Evaluation of N-nonyl-deoxygalactonojirimycin as a pharmacological chaperone for human GM1 gangliosidosis leads to identification of a feline model suitable for testing enzyme enhancement therapy
Molecular Genetics and Metabolism·2012· 43 citedOpen Access
Identification and Characterization of Ambroxol as an Enzyme Enhancement Agent for Gaucher Disease
Journal of Biological Chemistry·2009· 329 citedOpen Access
Cover Picture: Identification of Pharmacological Chaperones for Gaucher Disease and Characterization of Their Effects on β‐Glucocerebrosidase by Hydrogen/Deuterium Exchange Mass Spectrometry (ChemBioChem 16/2008)
ChemBioChem·2008· 1 citedOpen Access
Identification of Pharmacological Chaperones for Gaucher Disease and Characterization of Their Effects on β‐Glucocerebrosidase by Hydrogen/Deuterium Exchange Mass Spectrometry
ChemBioChem·2008· 74 citedOpen Access
100. Effects of novel β-glucocerebrosidase enhancers and pharmacological chaperones on protein stability/dynamics probed by hydrogen–deuterium exchange mass spectrometry
Molecular Genetics and Metabolism·2008
Pyrimethamine as a Potential Pharmacological Chaperone for Late-onset Forms of GM2 Gangliosidosis
Journal of Biological Chemistry·2007· 177 citedOpen Access

Frequent Co-authors

Michael B. Tropak(6), Don J. Mahuran(6), Gustavo Maegawa(5), Brigitte Rigat(5), G. Kornhaber(3), Yoshitomo Hamuro(3), Eric D. Brown(3), Joe T.R. Clarke(2), Jan Blanchard(2), Cecilia Murphy(2), Steven Tuske(2), Stephen J. Coales(2), Maria Fuller(1), Deepangi Pandit(1), Liangiie Tang(1), Tracy Stockley(1), Fernando Kok(1), Ellen Crushell(1), Daphne Benedict(1), John W. Callahan(1)